porphyria cutanea tarda symptomatica

Porphyria cutanea tarda symptomatica, also known as cutaneous porphyria, is a condition characterized by increased production and excretion of porphyrins, which are components of heme found in red blood cells. This disorder typically affects males and often appears later in life, between the fourth and eighth decades.1

The primary symptom is fragile and light-sensitive skin, particularly on exposed areas. Liver dysfunction can also be present, especially in individuals with chronic alcoholism. Abstinence from alcohol often leads to significant improvement or resolution of symptoms. While the tendency to develop this form of porphyria may be inherited, it can also be acquired through intoxications. Treatment focuses on managing symptoms and preventing skin injury, as there is no specific cure.1