hypoplastic left heart syndrome
Quick Summary
Hypoplastic left heart syndrome (HLHS) is a serious congenital heart defect where the left side of the heart, including the left ventricle and aorta, is underdeveloped. This severe underdevelopment significantly compromises the body's blood flow. Infants born with HLHS typically survive only a few days without intervention. In some cases, only one heart chamber develops adequately, and survival depends on compensatory abnormalities like a persistent ductus arteriosus or a septal defect. HLHS is a cyanotic type of congenital heart disease, meaning it can lead to a bluish discoloration of the skin due to a lack of oxygenated blood.12
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- congenital heart disease
One example is hypoplastic left heart syndrome, a very serious condition in which the left ventricle and other structures are underdeveloped, severely compromising blood flow through the body. Fortunately, surgical advances have made it possible to correct many defects, so that some patients who once would have succumbed…
Read MoreOne example is hypoplastic left heart syndrome, a very serious condition in which the left ventricle and other structures are underdeveloped, severely compromising blood flow through the body. Fortunately, surgical advances have made it possible to correct many defects, so that some patients who once would have succumbed…
Read More 
cardiovascular diseaseAbnormalities of individual heart chambersIn hypoplastic left heart syndrome, the left-sided heart chambers, including the aorta, are underdeveloped. Infants born with this condition rarely survive more than two or three days. In other cases, only one chamber develops adequately. Survival often depends on the presence of associated compensatory abnormalities, such…
Read MoreIn hypoplastic left heart syndrome, the left-sided heart chambers, including the aorta, are underdeveloped. Infants born with this condition rarely survive more than two or three days. In other cases, only one chamber develops adequately. Survival often depends on the presence of associated compensatory abnormalities, such…
Read More